Il sagit dune maladie inflammatoire des gros vaisseaux qui touche surtout les femmes. It is a relatively rare disease, which presents with a wide spectrum of clinical features. The authors evaluate the usefulness of magnetic resonance mr imaging in the diagnosis of takayasu arteritis ta. Takayasus arteritis tak is a form of vasculitisa family of rare disorders characterized by inflammation of the blood vessels, which can restrict blood flow and damage vital organs and tissues. Examination showed a difference of 40 mm hg in systolic blood pressure between the 2 arms, together. Histological examination suggested takayasu s disease in 11 patients whereas the roentgenologic. To evaluate prospectively the clinical features, angiographic findings, and response to treatment of patients with takayasu arteritis. Aim of this report was to describe four children two girls with ta, as well as summarizing main published studies. Takayasus arteritis american college of rheumatology.
Ta occurs most commonly in female patients in the second and third decades of life, but has also been reported in children as young as 24 months of age 1. A 19yearold woman presented with a 4month history of fatigue, weight loss, and thrombocytosis. The arterial revascularization should also be considered if necessary and regular monitoring is mandatory. Other articles where takayasus disease is discussed. Mr images of 77 patients with ta 74 women, three men were obtained with a 1.
Takayasu arteritis in children europe pmc article europe pmc. Symptoms, including diminished or absent pulses in the arms. We report a case of a 28yearold female with no known comorbidity, who presented with back pain along with. Takayasuarteritis arteritis, takayasu pulseless disease takayasusyndrom. Ultrasound of the carotid and subclavian arteries can aid in early diagnosis of the disease. The mean age at presentation of our cases was 11 years range. Takayasu arteritis is a rare, systemic, inflammatory largevessel vasculitis of unknown etiology that most commonly affects women of childbearing age. The mean age at presentation of our cases was 11 years range 815. Initial roentgenologic clinical, and histologic findings were evaluated and compared with final diagnosis. Takayasus arteritis also known as, aortic arch syndrome, nonspecific aortoarteritis, and pulseless disease. Takayasu disease definition of takayasu disease by medical. Takayasu arteritis, with variants called pulseless disease, branchial arteritis, and giantcell arteritis of the aorta, involves principally the thoracic aorta chest portion and the adjacent segments of its large branches.
Ascending aortic aneurysm associated with aortic insuf. Cest une aortoarterite non specifique touchant laorte, les arteres qui en naissent et les arteres pulmonaires. Mk, pasquier g, herreman f, bonnin a, fouchard j, houille f. Hong cy, yung ys, choi jy, sul jh, lee ks, cha sh, et al. The disease results from an attack by the bodys own immune system, causing inflammation in the walls of arteries. Takayasus arteritis, also called tak, is a rare form of vasculitis disease involving inflammation in the walls of the largest arteries in the body. Takayasus arteritis is a largevessel vasculitis occurring mainly in adolescent girls and young women. Takayasu arteritis in korean children clinical report of seventy cases. Takayasu arteritis ta is a rare chronic inflammatory disease of the aorta and its major branches.
Arterite a cellules geantes arterite temporale arterite granulomateus. Inpatient care is limited to managing acute manifestations of the disease, which usually result in complications from organ failure, stroke, pregnancy, seizures, and intracranial hemorrhage. Aortic valve replacement for acute takayasus disease. The macaroni sign of takayasus arteritis the journal of. Examination showed a difference of 40 mm hg in systolic blood pressure between the 2 arms. Takayasu s arteritis also known as, aortic arch syndrome, nonspecific aortoarteritis, and pulseless disease.
Takayasu arteritis ta is a large vessel vasculitis that usually affects young female patients during the second and third decades of life, but has been reported in children as young as 24 months of age. Dans une etude nordamericaine, lincidence est estimee a 2,6 casmillionsan1. Takayasu arteritis ta is a large vessel vasculitis affecting mainly the aorta and its major branches. It is seen predominantly in females during the second and third decades of life, although it can occur in childhood. To date, familial cases of ta have been considered rare. Tak affects the aorta and its main branches, which carry blood from the heart to the rest of the body. Intensive care unit icu admission is indicated for patients with critical deterioration. Takayasu arteritis in children pediatric rheumatology. Takayasu arteritis ta is a chronic inflammatory largevessel vasculitis of the aorta and its major branches. Histological examination suggested takayasus disease in 11 patients whereas the roentgenologic. Back pain is, however, rarely described to be a presenting symptom of ta.
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